BACKGROUND: Most of the patients with type 1 and V hyperlipoproteinemia HLP present with symptoms and signs of acute pancreatitis due to marked elevation of triglycerides, but this baby presented with a chest infection, which was later diagnosed as type V HLP on laboratory workup. ...On examination his heart rate was 102 beats min, respiratory rate was 55 breaths min and temperature was within the normal range, provisional diagnosis of Pneumonia was made. ...